Chronic Thromboembolic Pulmonary Hypertension (CTEPH) presenting as a right atrial myxoma- A case report and review of the literature

Document Type : Case Report

Authors

1 Ross University School of Medicine, Barbados

2 College of Biomedical Sciences, Larkin University, Miami, Florida, USA JAS Medical Management, Miramar, Florida, USA

3 Dr. Kiran C. Patel College of Osteopathic Medicine, Nova Southeastern University, Fort Lauderdale, Florida, USA

4 Biological Sciences Department, Broward College, Davie, Florida, USA

5 College of Biomedical Sciences, Larkin University, Miami, Florida, USA

Abstract

Background: Pulmonary hypertension arise from an increase in resistance within the pulmonary vasculature, leading to consequences such as hypoxia, hypoxemia, and right heart failure. The underlying causes of this increased resistance are diverse and classified using the World Health Organization (WHO) classification system. One specific etiology is chronic thromboembolic pulmonary hypertension or simply CTEPH.
Case presentation: This case report focuses on a 42-year-old African American cisgender female who presented with a deep vein thrombosis in her left leg and shortness of breath. Further investigation revealed a large mass in her right atrium during a bedside echocardiogram, suggestive of a possible right atrial myxoma. This patient subsequently underwent median sternotomy with thrombectomy.
Discussion: As a sequela to this clinical presentation, our patient developed pulmonary hypertension. This report delves into the challenges and complexities involved in diagnosing and treating pulmonary hypertension, while also highlighting the unique presentation of this patient.

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Main Subjects

References

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Journal of Preventive and Complementary Medicine
Volume 2, Issue 4
September 2023
Pages 209-218

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History

  • Receive Date: 20 July 2023
  • Revise Date: 15 September 2023
  • Accept Date: 20 September 2023

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